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eISSN: 2300-8660
ISSN: 0031-3939
Pediatria Polska - Polish Journal of Paediatrics
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abstract:
Review paper

Anomalous left coronary artery from the pulmonary artery - what we know about the disease 90 years after its discovery by Bland, White, and Garland

Marcin Wasilewski
1
,
Aleksandra Moszura
2
,
Julia Skwara
3
,
Maciej Nowicki
3
,
Dawid Barański
4
,
Anna Salińska
5
,
Gustaw Laskowski
6
,
Natalia Dąbrowska
7
,
Piotr Węgrzyn
6
,
Konstancja Węgrzyn
6
,
Agnieszka Góra
8
,
Paweł Kurzyna
9

  1. Department of Cardiovascular Diseases, Centre of Postgraduate Medical Education, Warsaw, Poland
  2. Department of Cardiology, Polish-Mother’s Memorial Hospital Research Institute, Łódź, Poland
  3. National Medical Institute of the Ministry of the Interior and Administration, Warsaw, Poland
  4. Jerzy Popiełuszko Bielański Hospital- Independent Public Healthcare Centre, Poland
  5. Mazowiecki Szpital Brodnowski Warsaw, Poland
  6. Central Clinical Hospital, Warsaw, Poland
  7. Infant Jesus Clinical Hospital, Warsaw, Poland
  8. Medical University of Warsaw, Warsaw, Poland
  9. Chair and Department of Pulmonary Circulation, Thromboembolic Diseases and Cardiology, Center of Postgraduate Medical Education, European Health Centre, ERN-LUNG Member, Otwock, Poland
Pediatr Pol 2024; 99 (4)
Online publish date: 2024/10/16
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Anomalous left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital coronary anomaly associated with a mortality rate of 90% within the first year of life, with diagnosis occurring in only 10–15% of patients during adulthood. ALCAPA is subdivided into infant type and adult type. While angiography remains the diagnostic gold standard, echocardiography serves as a convenient, non-invasive, and highly reliable initial step in suspected cases of ALCAPA. Computed tomography and magnetic resonance imaging are also capable of providing definitive diagnosis. Surgical management aims to establish a dual-coronary system through various techniques, with goals including gradual improvement in left ventricular function and reduction in mitral regurgitation. In selected cases, consideration may also be given to mitral valvuloplasty or placement of an implantable cardioverter defibrillator. Postoperatively, patients should undergo regular follow-up evaluations to monitor cardiac function and detect any complications.
keywords:

artery, Bland-White-Garland syndrome, adult congenital heart disease

 
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