Case report<BR>Blue rubber bleb naevus syndrome – case report

Zbigniew Samochocki; Jowita Dejewska; Romana Bogusławska-Walecka; Stanisław Wojtuń; Robert Koktysz

eISSN: 2299-0046
ISSN: 1642-395X

Advances in Dermatology and Allergology/Postępy Dermatologii i Alergologii

Current issue Archive Manuscripts accepted About the journal Editorial board Reviewers Abstracting and indexing Subscription Contact Instructions for authors Publication charge Ethical standards and procedures

Editorial System

Submit your Manuscript

Editorial Policies

Sarajevo Declaration on Integrity and Visibility of Scholarly Publications

2/2008
vol. 25

Send email

Copy url:

abstract:

Case report
Blue rubber bleb naevus syndrome – case report

Zbigniew Samochocki

,

Jowita Dejewska

,

Romana Bogusławska-Walecka

,

Stanisław Wojtuń

,

Robert Koktysz

Post Dermatol Alergol 2008; XXV, 2: 83–86

Online publish date: 2008/04/23

View full text Get citation

Blue rubber bleb naevus syndrome (BRBNS) is an uncommon and rare disorder characterised by multiple venous malformations of the skin and many internal organs. Angiomas involving internal organs may be the cause of bleeding resulting in profound anaemia, acute haemorrhage, intussusception or even death. The skin lesions are usually multiple, disseminated, generally small, bluish-purple, soft vascular tumours with rubber-like texture (which explains the syndrome’s full name). The most common extracutaneous localization of vascular malformations is the gastrointestinal tract, and particularly the small intestine. We report a case of BRBNS in a 52-year old woman, with disseminated skin changes which developed over approximately two years, predominating on the upper trunk and in the oral cavity. The histological findings were characteristic for the syndrome. No pathological findings were present on examination of internal organs.

keywords:

Case reportBlue rubber bleb naevus syndrome – case report

Zbigniew Samochocki , Jowita Dejewska , Romana Bogusławska-Walecka , Stanisław Wojtuń , Robert Koktysz

blue rubber bleb naevus syndrome, venous malformation

Case report
Blue rubber bleb naevus syndrome – case report

Zbigniew Samochocki

,

Jowita Dejewska

,

Romana Bogusławska-Walecka

,

Stanisław Wojtuń

,

Robert Koktysz