Complex grade III astrocytoma with granular cells and PXA features in a patient with tuberous sclerosis complex (Bourneville-Pringle syndrome) – case report and review of literature

Anna Mucha-Małecka; Krzysztof Małecki; Michał Kurzyński; Dariusz Adamek; Beata Biesaga; Konrad Urbanek; Aleksandra Grela-Wojewoda; Elżbieta Pluta; Anna Patla; Maciej Modrzejewski; Paweł Blecharz; Natalia Amrogowicz

doi:10.5114/pjp.2021.109522

eISSN: 2084-9869
ISSN: 1233-9687

Polish Journal of Pathology

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2/2021
vol. 72

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abstract:

Case report

Complex grade III astrocytoma with granular cells and PXA features in a patient with tuberous sclerosis complex (Bourneville-Pringle syndrome) – case report and review of literature

Anna Mucha-Małecka

¹

,

Krzysztof Małecki

^{2, 3}

,

Michał Kurzyński

⁴

,

Dariusz Adamek

⁵

,

Beata Biesaga

^{6, 7}

,

Konrad Urbanek

¹

,

Aleksandra Grela-Wojewoda

⁸

,

Elżbieta Pluta

¹

,

Anna Patla

¹

,

Maciej Modrzejewski

¹

,

Paweł Blecharz

⁹

,

Natalia Amrogowicz

¹⁰

Department of Radiotherapy, Maria Sklodowska-Curie National Research Institute of Oncology, Krakow Branch, Poland
Department of Radiotherapy for Children and Adults, University Children’s Hospital of Krakow, Poland
Jagiellonian University in Cracow, Faculty of Health Sciences, Krakow, Poland
Amethyst Radiotherapy Poland, Krakow, Poland
Department of Pathology, Jagiellonian University Medical College, Krakow, Poland
Center for Translational Research and Molecular Biology of Cancer, Maria Sklodowska-Curie National Research Institute of Oncology, Gliwice Branch, Poland
Department of Tumour Pathology, Maria Sklodowska-Curie National Research Institute of Oncology, Krakow Branch, Poland
Department of Clinical Oncology, Maria Sklodowska-Curie National Research Institute of Oncology, Krakow Branch, Poland
Gynecologic Oncology Department, Maria Sklodowska-Curie National Research Institute of Oncology, Krakow Branch, Poland
I Radiation and Clinical Oncology Department, Maria Sklodowska-Curie National Research Institute of Oncology, Gliwice Branch, Poland

Pol J Pathol 2021; 72 (2): 180-184

DOI: https://doi.org/10.5114/pjp.2021.109522

Online publish date: 2021/09/30

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AMA

Mucha-Małecka A, Małecki K, Kurzyński M, et al. Complex grade III astrocytoma with granular cells and PXA features in a patient with tuberous sclerosis complex (Bourneville-Pringle syndrome) – case report and review of literature. Polish Journal of Pathology. 2021;72(2):180-184. doi:10.5114/pjp.2021.109522.

APA

Mucha-Małecka, A., Małecki, K., Kurzyński, M., Adamek, D., Biesaga, B.,  & Urbanek, K. et al. (2021). Complex grade III astrocytoma with granular cells and PXA features in a patient with tuberous sclerosis complex (Bourneville-Pringle syndrome) – case report and review of literature. Polish Journal of Pathology, 72(2), 180-184. https://doi.org/10.5114/pjp.2021.109522

Chicago

Mucha-Małecka, Anna, Krzysztof Małecki, Michał Kurzyński, Dariusz Adamek, Beata Biesaga, Konrad Urbanek,  and Aleksandra Grela-Wojewoda et al. 2021. "Complex grade III astrocytoma with granular cells and PXA features in a patient with tuberous sclerosis complex (Bourneville-Pringle syndrome) – case report and review of literature". Polish Journal of Pathology 72 (2): 180-184. doi:10.5114/pjp.2021.109522.

Harvard

Mucha-Małecka, A., Małecki, K., Kurzyński, M., Adamek, D., Biesaga, B., Urbanek, K., Grela-Wojewoda, A., Pluta, E., Patla, A., Modrzejewski, M., Blecharz, P.,  and Amrogowicz, N. (2021). Complex grade III astrocytoma with granular cells and PXA features in a patient with tuberous sclerosis complex (Bourneville-Pringle syndrome) – case report and review of literature. Polish Journal of Pathology, 72(2), pp.180-184. https://doi.org/10.5114/pjp.2021.109522

MLA

Mucha-Małecka, Anna et al. "Complex grade III astrocytoma with granular cells and PXA features in a patient with tuberous sclerosis complex (Bourneville-Pringle syndrome) – case report and review of literature." Polish Journal of Pathology, vol. 72, no. 2, 2021, pp. 180-184. doi:10.5114/pjp.2021.109522.

Vancouver

Mucha-Małecka A, Małecki K, Kurzyński M, Adamek D, Biesaga B, Urbanek K et al. Complex grade III astrocytoma with granular cells and PXA features in a patient with tuberous sclerosis complex (Bourneville-Pringle syndrome) – case report and review of literature. Polish Journal of Pathology. 2021;72(2):180-184. doi:10.5114/pjp.2021.109522.

PlumX metrics:

Tuberous sclerosis complex (Bourneville-Pringle syndrome) is a rare genetic condition included in the group of diseases called phakomatoses. Most of the patients are diagnosed with abnormalities within the central nervous system and tend to develop tumors more frequently, especially gliomas. We present a case of 50-year-old patient suffering from tuberous sclerosis complex, who had been diagnosed with pleomorphic xanthoastrocytoma (PXA). The patient underwent surgery and adjuvant radiotherapy and has remained free from local recurrence for 5 years.

keywords:

Complex grade III astrocytoma with granular cells and PXA features in a patient with tuberous sclerosis complex (Bourneville-Pringle syndrome) – case report and review of literature

Anna Mucha-Małecka 1 , Krzysztof Małecki 2, 3 , Michał Kurzyński 4 , Dariusz Adamek 5 , Beata Biesaga 6, 7 , Konrad Urbanek 1 , Aleksandra Grela-Wojewoda 8 , Elżbieta Pluta 1 , Anna Patla 1 , Maciej Modrzejewski 1 , Paweł Blecharz 9 , Natalia Amrogowicz 10

pleomorphic xanthoastrocytoma, tuberous sclerosis complex, Bourneville-Pringle syndrome, surgery, radiotherapy