DZIELIMY SIĘ DOŚWIADCZENIEM<br>Mitral insufficiency and aortic arch aneurysm in a woman with Marfan syndrome treated twice in the cardiac surgery unit

Agata Bilewska; Mariusz Kuśmierczyk; Ilona Michałowska; Piotr Hoffman; Jacek M. Różański

eISSN: 1897-4252
ISSN: 1731-5530

Kardiochirurgia i Torakochirurgia Polska/Polish Journal of Thoracic and Cardiovascular Surgery

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3/2009
vol. 6

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abstract:

DZIELIMY SIĘ DOŚWIADCZENIEM
Mitral insufficiency and aortic arch aneurysm in a woman with Marfan syndrome treated twice in the cardiac surgery unit

Agata Bilewska

,

Mariusz Kuśmierczyk

,

Ilona Michałowska

,

Piotr Hoffman

,

Jacek M. Różański

Kardiochirurgia i Torakochirurgia Polska 2009; 6 (3): 289–292

Online publish date: 2009/09/23

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AMA

Bilewska A, Kuśmierczyk M, Michałowska I, Hoffman P, Różański J. DZIELIMY SIĘ DOŚWIADCZENIEMMitral insufficiency and aortic arch aneurysm in a woman with Marfan syndrome treated twice in the cardiac surgery unit. Kardiochirurgia i Torakochirurgia Polska/Polish Journal of Thoracic and Cardiovascular Surgery. 2009;6(3):289-292.

APA

Bilewska, A., Kuśmierczyk, M., Michałowska, I., Hoffman, P.,  & Różański, J. (2009). DZIELIMY SIĘ DOŚWIADCZENIEMMitral insufficiency and aortic arch aneurysm in a woman with Marfan syndrome treated twice in the cardiac surgery unit. Kardiochirurgia i Torakochirurgia Polska/Polish Journal of Thoracic and Cardiovascular Surgery, 6(3), 289-292.

Chicago

Bilewska, Agata, Mariusz Kuśmierczyk, Ilona Michałowska, Piotr Hoffman,  and Jacek M. Różański. 2009. "DZIELIMY SIĘ DOŚWIADCZENIEMMitral insufficiency and aortic arch aneurysm in a woman with Marfan syndrome treated twice in the cardiac surgery unit". Kardiochirurgia i Torakochirurgia Polska/Polish Journal of Thoracic and Cardiovascular Surgery 6 (3): 289-292.

Harvard

Bilewska, A., Kuśmierczyk, M., Michałowska, I., Hoffman, P.,  and Różański, J. (2009). DZIELIMY SIĘ DOŚWIADCZENIEMMitral insufficiency and aortic arch aneurysm in a woman with Marfan syndrome treated twice in the cardiac surgery unit. Kardiochirurgia i Torakochirurgia Polska/Polish Journal of Thoracic and Cardiovascular Surgery, 6(3), pp.289-292.

MLA

Bilewska, Agata et al. "DZIELIMY SIĘ DOŚWIADCZENIEMMitral insufficiency and aortic arch aneurysm in a woman with Marfan syndrome treated twice in the cardiac surgery unit." Kardiochirurgia i Torakochirurgia Polska/Polish Journal of Thoracic and Cardiovascular Surgery, vol. 6, no. 3, 2009, pp. 289-292.

Vancouver

Bilewska A, Kuśmierczyk M, Michałowska I, Hoffman P, Różański J. DZIELIMY SIĘ DOŚWIADCZENIEMMitral insufficiency and aortic arch aneurysm in a woman with Marfan syndrome treated twice in the cardiac surgery unit. Kardiochirurgia i Torakochirurgia Polska/Polish Journal of Thoracic and Cardiovascular Surgery. 2009;6(3):289-292.

Marfan syndrome is an autosomal dominant disorder of the connective tissue. Mutation in the fibrillin gene locus is believed to be responsible for impaired structural integrity of the elastin network. Symptoms of Marfan syndrome involve the skeletal, ocular and cardiovascular systems.
We report a case of a 26-year-old woman with Marfan syndrome referred for surgical treatment because of mitral insufficiency and aortic aneurysm. The patient was operated on twice. As a 12-year-old girl she underwent aortic root replacement with composite graft (Bentall-de Bono procedure). After 7 years she was reoperated on. The third operation involved mitral valve replacement and resection of the ascending aorta and the arch due to a large aneurysm located distally to the previous anastomosis. The cardiopulmonary bypass was initiated through the innominate artery. A few weeks after the operation the patient required vacuum-assisted therapy due to sternal wound infection.

keywords:

DZIELIMY SIĘ DOŚWIADCZENIEMMitral insufficiency and aortic arch aneurysm in a woman with Marfan syndrome treated twice in the cardiac surgery unit

Agata Bilewska , Mariusz Kuśmierczyk , Ilona Michałowska , Piotr Hoffman , Jacek M. Różański

Marfan syndrome, aortic aneurysm

DZIELIMY SIĘ DOŚWIADCZENIEM
Mitral insufficiency and aortic arch aneurysm in a woman with Marfan syndrome treated twice in the cardiac surgery unit

Agata Bilewska

,

Mariusz Kuśmierczyk

,

Ilona Michałowska

,

Piotr Hoffman

,

Jacek M. Różański