eISSN: 1897-4309
ISSN: 1428-2526
Contemporary Oncology/Współczesna Onkologia
Current issue Archive Manuscripts accepted About the journal Supplements Addendum Special Issues Editorial board Reviewers Abstracting and indexing Subscription Contact Instructions for authors Publication charge Ethical standards and procedures
Editorial System
Submit your Manuscript
SCImago Journal & Country Rank
5/2007
vol. 11
 
Share:
Share:
abstract:

Malignant peripheral nerve sheeth tumors (MPNST) – case report

Ewa Ziółkowska
,
Mariusz Mross
,
Marta Biedka
,
Roman Makarewicz

Współczesna Onkologia (2007) vol. 11; 5 (247-251)
Online publish date: 2007/07/16
View full text Get citation
 
Malignant peripheral nerve sheath tumours (MPNST) are a rare entity accounting for 5%-10% f soft-tissue sarcomas. They mostly arise de novo, especially in patients suffering from neurofibromatosis. MPNST mostly arise in the trunk (50%), followed by the extremities (30%) and the head and neck region (20%). Distant metastases are common (40%-80%) and they are most frequently found in the lung and liver. Less common locations are: bone, soft tissue, adrenal glands, brain, ovaries and kidneys. The main treatment is wide surgical excision, which is reported as paramount to local control with adjuvant radiotherapy and brachytherapy.
keywords:

sarcoma, malignant peripheral nerve sheath tumours (MPNST), treatment

Quick links
© 2024 Termedia Sp. z o.o.
Developed by Bentus.