Malignant peripheral nerve sheeth tumors (MPNST) – case report

Ewa Ziółkowska; Mariusz Mross; Marta Biedka; Roman Makarewicz

eISSN: 1897-4309
ISSN: 1428-2526

Contemporary Oncology/Współczesna Onkologia

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5/2007
vol. 11

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abstract:

Malignant peripheral nerve sheeth tumors (MPNST) – case report

Ewa Ziółkowska

,

Mariusz Mross

,

Marta Biedka

,

Roman Makarewicz

Współczesna Onkologia (2007) vol. 11; 5 (247-251)

Online publish date: 2007/07/16

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Malignant peripheral nerve sheath tumours (MPNST) are a rare entity accounting for 5%-10% f soft-tissue sarcomas. They mostly arise de novo, especially in patients suffering from neurofibromatosis. MPNST mostly arise in the trunk (50%), followed by the extremities (30%) and the head and neck region (20%). Distant metastases are common (40%-80%) and they are most frequently found in the lung and liver. Less common locations are: bone, soft tissue, adrenal glands, brain, ovaries and kidneys. The main treatment is wide surgical excision, which is reported as paramount to local control with adjuvant radiotherapy and brachytherapy.

keywords:

Malignant peripheral nerve sheeth tumors (MPNST) – case report

Ewa Ziółkowska , Mariusz Mross , Marta Biedka , Roman Makarewicz

sarcoma, malignant peripheral nerve sheath tumours (MPNST), treatment

Ewa Ziółkowska

,

Mariusz Mross

,

Marta Biedka

,

Roman Makarewicz