en POLSKI
eISSN: 2300-8660
ISSN: 0031-3939
Pediatria Polska - Polish Journal of Paediatrics
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6/2018
vol. 93
 
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abstract:
Case report

Nephropathy in the course of IgA vasculitis – case report

Katarzyna Dyga
,
Majka Jaszczura
,
Piotr Adamczyk
,
Omar Bjanid
,
Aurelia Morawiec-Knysak
,
Maria Szczepańska

Pediatr Pol 2018; 93 (6): 492–495
Online publish date: 2019/01/07
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IgA vasculitis (IgAV), formerly known as Henoch-Schönlein purpura (HSP), is the most common form of systemic vasculitis in children. Nephrological symptoms in the course of the disease are observed in 30–50% of children. The prognosis for maintaining normal kidney function is good in most patients; however, it depends on the primary clinical manifestation. Our aim was to present a case of a girl with nephropathy in the course of IgAV in the form of nephritic-nephrotic syndrome, who, despite early and intensive immunosuppressive treatment, revealed development of end-stage renal failure (ESRF) within two years. We also discuss the treatment of severe nephropathy in the course of IgAV, in accordance with current recommendations, which still remains a great challenge and does not guarantee slower progression of the disease.
keywords:

children, IgA vasculitis, nephropathy