Prenatal diagnosis of a unique scimitar syndrome variant – a case report

Justin Kochanski; Diana Bardo; Luis Goncalves; Chris Lindblade

doi:10.5114/pcard.2019.90997

eISSN: 2449-6731
ISSN: 2449-6723

Prenatal Cardiology

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abstract:

Case report

Prenatal diagnosis of a unique scimitar syndrome variant – a case report

Justin J. Kochanski

¹

,

Diana Bardo

²

,

Luis Goncalves

²

,

Chris Lindblade

³

Creighton University School of Medicine, Phoenix, USA
Department of Radiology, Phoenix Children’s Hospital, Phoenix, USA
Department of Cardiology, Phoenix Children’s Hospital, Phoenix, USA

Prenat Cardio 2019; 9(1): 42-46

DOI: https://doi.org/10.5114/pcard.2019.90997

Online publish date: 2019/12/19

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Scimitar syndrome is a rare condition characterised by abnormal pulmonary venous return to the inferior vena cava. It is associated with various cardiopulmonary malformations such as atrial-septal defects, aorticopulmonary collateral vessels, and pulmonary hypoplasia. Diagnosis is typically within the first few months of life. We report a unique case of scimitar syndrome that was diagnosed prenatally using multiple imaging modalities. In addition to two right-sided scimitar veins draining into the suprahepatic inferior vena cava, this patient was found to have horseshoe lung morphology with right pulmonary hypoplasia, a perimembranous ventricular septal defect, sequestered lung tissue, and an aorticopulmonary collateral vessel arising from the descending aorta. The prenatal diagnosis allowed for timely medical and surgical intervention in the postnatal period, which is detailed in this report.

keywords:

Prenatal diagnosis of a unique scimitar syndrome variant – a case report

Justin J. Kochanski 1 , Diana Bardo 2 , Luis Goncalves 2 , Chris Lindblade 3

scimitar syndrome, foetal imaging, horseshoe lung, dextrocardia, sequestered lung

Justin J. Kochanski

¹

,

Diana Bardo

²

,

Luis Goncalves

²

,

Chris Lindblade

³