Quiz. Correct answer to the quiz. Check your diagnosis<br>Mesenchymal chondrosarcoma of the orbit: two cases and a brief review of the literature

Anna Szumera-Ciećkiewicz; Konrad Ptaszyński; Piotr Grabowski; Romuald Krajewski; Małgorzata Tacikowska

eISSN: 2084-9869
ISSN: 1233-9687

Polish Journal of Pathology

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1/2012
vol. 63

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abstract:

Quiz. Correct answer to the quiz. Check your diagnosis
Mesenchymal chondrosarcoma of the orbit: two cases and a brief review of the literature

Anna Szumera-Ciećkiewicz

,

Konrad Ptaszyński

,

Piotr Grabowski

,

Romuald Krajewski

,

Małgorzata Tacikowska

Online publish date: 2012/04/24

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Mesenchymal chondrosarcoma (MChS) is a rare, high-grade malignant tumor which occurs both in the bone and soft tissue. The extraskeletal location comprises one third of all MChS and in review of the up-to-date literature, about 30 cases of the orbital involvement were found. The authors present clinical, radiological and pathological findings of two cases of MChS of the orbit occurring in young adult females: primary extraskeletal MChS of the orbit and skeletal MChS of the ethmomaxillary complex with secondary orbit involvement. The histopathological examination revealed a characteristic biphasic pattern composed of small round to spindle-shaped cells, mimicking Ewing sarcoma family of tumors, with areas of a haemangiopericytoma-like pattern and admixed cartilage foci. One of the patients had local recurrence 3 years after initial surgical removal. Subsequently, she underwent enucleation followed by chemotherapy. The other patient had a biopsy and debulking resection of the tumor and started chemotherapy. Ten months follow-up of this patient show no evidence of metastasis.

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Quiz. Correct answer to the quiz. Check your diagnosisMesenchymal chondrosarcoma of the orbit: two cases and a brief review of the literature

Anna Szumera-Ciećkiewicz , Konrad Ptaszyński , Piotr Grabowski , Romuald Krajewski , Małgorzata Tacikowska

mesenchymal chondrosarcoma, chondrosarcoma, orbit, differential diagnosis

Quiz. Correct answer to the quiz. Check your diagnosis
Mesenchymal chondrosarcoma of the orbit: two cases and a brief review of the literature

Anna Szumera-Ciećkiewicz

,

Konrad Ptaszyński

,

Piotr Grabowski

,

Romuald Krajewski

,

Małgorzata Tacikowska